Yuli 2021: Beta-thalassaemia cuta ce ta gado ta hanyar maye gurbi a cikin kwayar halittar da ke da hannu wajen samar da wani bangaren haemoglobin, furotin da ke jigilar iskar oxygen a cikin jiki. Wadannan maye gurbi ko dai sun haramta ko iyakance samuwar haemoglobin, wanda ke haifar da karancin jajayen kwayoyin halittar jinin da suka balaga da anemia mai dagewa, da kuma wuce gona da iri.
Maye gurbin da ke haifar da beta thalassaemia yana shafar kusan mutane miliyan 80-90 a duk duniya, ko kuma kusan kashi 1.5 na yawan jama'a.
Yara akai-akai suna gadon maye gurbi daga iyayen da ke ɗauke da cutar amma ba su nuna alamun yanayin ba. Yaron yana da yuwuwar kashi 25% na samun beta-thalassaemia da kuma damar 50% na kasancewa mai ɗaukar asymptomatic kamar iyayensu a cikin wannan yanayin.
Many individuals with beta-thalassemia need regular blood transfusions for the rest of their lives (transfusion-dependent thalassemia), which can cause a variety of health problems, including iron excess, which can harm the heart, liver, and endocrine system.
Wasu ƙila ba za su buƙaci ƙarin ƙarin jini na yau da kullun don tsira ba (wanda ya dogara da ƙarin ƙarin jini), amma duk da haka suna fama da thrombosis, hauhawar jini na huhu, gazawar koda, da ciwon ƙafafu, da sauran matsalolin lafiya.
Beta thalassaemia yana yaduwa da sauri fiye da kowane lokaci
People from the Mediterranean, the Middle East, North Africa, India, and Central and Southeast Asia have been reported to have the highest prevalence of beta thalassemia. As a result of the rise in modern migration, instances are increasingly sprouting up in more places.
Ƙasashen da ke kudancin Bahar Rum sun haɓaka albarkatu don magance karuwar buƙatun majinyatan beta-thalassemia. Yayin da masana kiwon lafiya da ’yan siyasa a Arewacin Turai da Yammacin Turai suka fahimci wannan yanayin, ba su da cikakkun bayanai game da faruwar cutar da yanayin. Yana da wahala a sanya lamarin don saka hannun jari a cikin yunƙurin magance matsalar ba tare da bayanai ba, yana sa ya yi wahala ga marasa lafiya su gano madaidaitan masu samarwa.
Beta-thalassemia & COVID-19
Jiyya don beta-thalassemia yana buƙatar ɗimbin ilimi da albarkatu, gami da amintaccen gudummawar jini. Cutar ta COVID-19 ta yi tasiri sosai kan samar da jini a duniya, wanda ya haifar da raguwar gudummawar jini a yawancin kasashen EU da batutuwa na musamman a kasashe masu tasowa da masu karamin karfi tare da karancin albarkatu da yawan marasa lafiya. Nisantar masu ba da gudummawa da ƙarancin iya aiki a wuraren bayar da gudummawa, da sarrafa jini da katsewar sarkar samar da kayayyaki, duk sun taimaka wajen raguwar gudummawar jini.
Sabbin tsarin kulawa na beta-thalassemia
Magani ɗaya tilo don beta-thalassemia a yanzu akwai shi shine dashen sel mai tushe, kodayake mutane da yawa ƙila ba za su cancanci ba. Kusan kashi 10 cikin XNUMX na marasa lafiyar da suka cancanci dasawa a zahiri suna samun ɗaya, saboda tsadar kuɗi ko rashin mai bayarwa. Wata dabarar dogon lokaci ita ce rigakafin ta hanyar tantancewa da ilimi, wanda ya tabbatar yana da inganci a ƙasashe da yawa.
Koyaya, ci gaba na baya-bayan nan a cikin yanayin jiyya ya ba da zaɓin da ake buƙata don magance anemia da beta-thalassaemia ke haifarwa da ƙyale majiyyata su zama ƙasa da dogaro ga ƙarin ƙwayoyin jini.