July 2021: Beta-thalassemia inzvimbo yekugara nhaka inokonzerwa nekuchinja kwemajini inobatanidzwa mukugadzirwa kwechinhu chehemoglobin, iyo protein inotakura oxygen mumuviri wese. Shanduko idzi dzinorambidza kana kudzora hemoglobin kuumbika, zvichikonzera kushomeka kwemasero matsvuku eropa uye kuenderera kweanemia, pamwe neyakawandisa iron.
Shanduko inokonzeresa beta thalassemia inokanganisa vangangoita mamirioni makumi masere kusvika makumi mapfumbamwe pasi rese, kana ingangoita 80 muzana yevagari.
Vana vanowanzogara nhaka yegene mutation kubva kuvabereki vanotakura asi vasingaratidzi zviratidzo zvemamiriro acho. Mwana ane 25% mukana wekuwana beta-thalassemia uye 50% mukana wekuve asymptomatic mutakuri sevabereki vake mumamiriro ezvinhu aya.
Many individuals with beta-thalassemia need regular blood transfusions for the rest of their lives (transfusion-dependent thalassemia), which can cause a variety of health problems, including iron excess, which can harm the heart, liver, and endocrine system.
Vamwe vangangoda kuwedzerwa kuwedzerwa nguva dzose kuti vararame (vasingawedzerwe ropa), asi zvakadaro vanorwara neprombombosis, hypertension, kutadza kweitsvo, uye maronda emakumbo, pakati pemamwe matambudziko ehutano.
Beta thalassemia iri kupararira nekukurumidza kupfuura nakare kose
People from the Mediterranean, the Middle East, North Africa, India, and Central and Southeast Asia have been reported to have the highest prevalence of beta thalassemia. As a result of the rise in modern migration, instances are increasingly sprouting up in more places.
Nyika dziri kumaodzanyemba kweMediterranean dzakasimudzira zviwanikwa zvekugadzirisa kudiwa kuri kukura kwevarwere ve beta-thalassemia. Nepo nyanzvi dzezvehutano uye vezvematongerwo enyika kuchamhembe nekumadokero kweEurope vachiziva maitiro aya, havana ruzivo rwakasimba nezve kuitika kwechirwere uye maitiro. Zvakaoma kugadzira nyaya yekudyara muzvirongwa zvekugadzirisa dambudziko pasina dhata, zvichiita kuti zviomere varwere kuona vakapi chaivo.
Beta-thalassemia & COVID-19
Kurapa kwe beta-thalassemia kunoda huwandu hweruzivo uye zviwanikwa, kusanganisira neropa rakachengeteka. Iyo COVID-19 denda yakave nesimba rakakura mukupa kweropa kwepasirese, zvichikonzera kudzikira kwemipiro yeropa munyika zhinji dzeEU uye nenyaya dzakasarudzika munyika dzichiri kusimukira nedzine mari shoma dzine zviwanikwa zvishoma uye kuwanda kwevarwere vanorwara. Kudzivisa kwevanopa uye kushomeka kwenzvimbo dzekupa zvipo, pamwe nekugadziriswa kweropa uye kukanganiswa kwecheni, zvese zvakabatsira mukudonhedzwa kweropa.
Hutsva nzira dzekurapa beta-thalassemia
Mhinduro chete yebeta-thalassemia iripo ndeye stem cell transplant, kunyangwe vanhu vazhinji vangave vasina kukodzera. Chete vangangoita gumi muzana yevarwere vanokodzera kuisirwa stem cell vanotowana imwe, nekuda kwemitengo yakawandisa kana kushaikwa kweanopa. Imwe nzira yenguva refu ndeyekudzivirira kuburikidza nekuongororwa kwevatakuri uye dzidzo, izvo zvakaratidza kuti zvinoshanda munyika dzakawanda.
Zvisinei, kufambira mberi kwechangobva kuitika muhutano hwekurapa kwakapa sarudzo dzinodikanwa dzekugadzirisa kupererwa neropa kunokonzerwa neBeta-thalassemia uye kubvumidza varwere kuti vasanyanya kuvimba neropa tsvuku reropa.